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저자들은 48세의 여자환자에서 진단된 원발성항인지질증후군에서 드물게 발생하는 대동맥 혈전증 1례를 경험하였기에 문헌 고찰과 함께 보고하는 바이다.


Antiphospholipid syndrome (APS) is an autoimmune hypercoagulability syndrome. The clinical feature of the antiphospholipid syndrome is characterized by venous or arterial thromboses, recurrent fetal losses and/or thrombocytopenia with evidence of antiphospholipid antibodies, namely lupus anticoagulant, anticardiolipin antibodies. Although APS is most commonly associated with systemic lupus erythematosus or related autoimmune disease (secondary APS), APS also has been identified in patients with vaso-occlusive disease without any other manifestations of connective tissue disease (primary APS). In primary APS, aortic thrombosis has been rarely reported. We report a case of thrombosis of abdominal aorta in primary APS.